Juvenile Xanthogranuloma

Irma Primawati

Abstract


Juvenile xanthogranuloma is the most common form of non-Langerhans-cells histiocytosis or non-X histiocytosis. Most often affecting infants and young children.

A case of  juvenile xanthogranuloma in a 3-month-old male infant has been reported. There were multiple, discrete, firm, red-brownish, orange nodules, round and oval in shape, well-defined, 0.5–2 cm in diameter, disseminated on his scalp, face, trunk, upper and lower extremities, also genitalia and some of them with ulceration on its surface. No mucous membrane and systemic involvement. Pathology result revealed Touton giant cells that characteristic to juvenile xanthogranuloma although the other diseases might contain these cells such as Hashimoto-Pritzker disease and dermatofibroma. Within few years, the lesions could regression spontaneously and leaving a flat, atrophic scar or an area of altered pigmentation.


Keywords


Juvenile xanthogranuloma, Touton giant cells, regression spontaneously

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References


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DOI: https://doi.org/10.33854/heme.v2i1.298

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